Ch 6 Review Questions

All of the following are involved in cherubism except one. which one is the exception? A. coronoid process B. condyle C. posterior mandible D. ascending ramus

B. Condyle

Patients with osteogenesis imperfecta may develop dental anomalies that closely resemble which of the following conditions? A. Amelogenesis Imperfecta B. Dentinogenesis Imperfecta C. Radicular Dentin Dysplasia D. Taurodontism

B. Dentinogenesis Imperfecta

Tori Mandibularis and Torus Palatinus are: A. sporadic trait B. inherited as an autosomal-dominant trait C. inherited as an autosomal-recessive trait D. more prevalent in males

B. Inherited as an autosomal-dominant trait

Which of the following tumors is potentially life threatening? A. neuroma B. Medullary Carcinoma of thyroid C. osteoma D. pheochromocytoma

B. Medullary Carcinoma of Thyroid

the characteristic finding in permanent teeth affected with coronal dentin dysplasia is: A. large, square pulp chambers in molars B. thistle-shaped pulp chambers in incisors C. crowns with amber color D. markedly short roots

B. Thistle shaped pulp chambers in incisors

Which of the following is NOT considered a component of MEN 2B syndrome? A. Pheochromocytoma B. Medullary Thyroid Carcinoma C. Multiple Mucosal Neuromas D. Bilateral acoustic neuromas

D. Bilateral acoustic neuromas

what is assessed by a patients karyotype? A. Protein B. RNA C. bone structure D. chromosomes

D. Chromosomes

Intestinal Polyps are the most significant clinical characteristics of which of the following syndromes? A. Gardner B. Ellis-Van Creveld C. Laband D. Cleidocranial Dysostosis

A. Gardner

premature loss of the mandibular incisor teeth may be seen in which of the following conditions? A. hypophosphatasia B. vitamin D- resistant rickets C. Down syndrome D. gorlin syndrome

A. Hypophosphatasia

Taurodontism is most often observed in: A. Native Americans B. Asians C. Europeans D. South Americans

A. Native Americans

Kostmann Syndrome is a variety of which of the following? A. Neutropenia B. Leukemia C. Osteogenesis D. Hemophilia

A. Neutropenia

Barr bodies are seen at the: A. Nuclear Periphery of all cells in woman B. periphery of the cytoplasm in all human cells C. Nuclear Periphery of all human cells D. periphery of the cytoplasm in all cells from women

A. Nuclear periphery of all cells in woman

Which of the following statements regarding Peutz-Jeghers syndrome is false? A. patients will develop adenomatous polyps of the gastrointestinal tract B. patients will develop peri oral pigmentation C. it is caused by an alteration in chromosome 19 D. all of the above are true

A. Patients will develop adenomatous polyps of the gastrointestinal tract

the order of the four stages of mitosis is: A. Prophase, Metaphase, Anaphase, Telophase B. Metaphase, Prophase, Telophase, Anaphase C. Anaphase, Metaphase, Telophase, Prophase D. prophase, telophase, metaphase, anaphase

A. Prophase, Metaphase, Anaphase, Telophase

In dentinogensis imperfecta type II, teeth have: A. roots that are short and thin B. dilacerated roots C. hard, dense dentin D. markedly brittle enamel

A. Roots that are short and thin

Both Gardner syndrome and Cleidocranial dysplasia may be associated with which of the following oral manifestations? A. Supernumerary teeth B. Osteomas of the mandible C. Multiple Odontogenic keratocysts of the jaw D. Premature exfoliation of mandibular incisor teeth

A. Supernumerary teeth

the Lyon hypothesis is demonstrated by: A. X-linked dominant traits B. X-linked recessive traits C. autosomal dominat traits D. autosomal recessive-traits

A. X-linked dominant trait

patients with an X-linked hereditary condition: A. are generally affected more severely if they are men B. are always XYY C. have cells with an extra Barr body D. are always woman

A. are generally affected more severely if they are men

the cause of all forms of labial and palatal clefting is considered to be: A. multifactorial B. environmental C. autosomal recessive D. autosomal dominat

A. multifactorial

which of the following is TRUE for Von Recklinghausen disease? A. patients may have gingival neurofibromas B. it is inherited as an autosomal-recessive trait C. patients experience a generalized whitening of the oral mucosa D. patients have multiple fibromatoses

A. patient may have gingival neurofibromas

All of the following are characteristics of ribosomes except one. which one is the exception? A. They are located in the nucleus B. they facilitate the formation of new proteins C. they are partly made of RNA D. they bind to tRNA molecules

A. they are located in the nucleus

cannon disease is also known as: A. white sponge nevus B. gingival fibromatosis C. chronic neutropenia D. cherubism

A. white sponge nevus

The karyotype of a patient with Turner syndrome shows: A. 43 Autosomes and XYY B. 44 autosomes and XO C. 44 Autosomes and XYY D. 44 autosomes and XXY

B. 44 autosomes and XO

Hypothetically, an autosomal-dominant trait would be clinically present in: A. 25% of the offspring of an affected parent B. 50% of the offspring of an affected parent C. 75% of the offspring of an affected parent D. only in males, never in female offspring.

B. 50% of the offspring of an affected parent

in all inherited varieties of gingival fibrzomatosis, the gingival enlargement is characterized by a marked: A. Alveolar Bone Hypertrophy B. Collagenization of the connective tissue C. Hyperplasia of the covering epithelium D. chronic inflammatory cellular infiltrate

B. Collagenization of the connective tissue

A gamete is the result of the process of: A. The S phase B. Meiosis C. Mitosis D. Prophase

B. Meiosis

which of the following components of the Peutz-Jeghers syndrome? A. Multiple Jaw Cysts B. multiple pigmented macule on the lower lip and mucosa C. Multiple nodules on the tip of the tongue D. multiple supernumerary teeth

B. Multiple Pigmented Macule's on the lower lip and mucosa

Bilateral acoustic neuromas are seen in which of the following syndromes? A. Neurofibromatosis Type I B. Neurofibromatosis Type II C. MEN 2B D. Cleidocranial Dysplasia

B. Neurofibromatosis Type II

Which of the following syndromes does not have gingival fibromatosis as a clinical feature? A. Leband B. Papillon-Lefevre C. Murray-Puretic-Drescher D. hypertrichosis, epilepsy, and mental retardation

B. Papillon-Lefevre

Trisomy 13 is also referred to as: A. Down Syndrome B. Patu Syndrome C. Gorlin Syndrome D. Gardner Syndrome

B. Patu Syndrome

which of the following is typically found in the MEN 2B syndrome? A. carcinoma of the pancreas B. pheochromocytoma C. basal cell carcinomas D. carcinoma of the colon

B. Pheochromocytoma

people with snow-capped amelogenis imperfecta have teeth with: A. Short, blunted roots B. white, hypocalcified enamel at the incisal and occlusal thirds C. a thin, brown enamel D. obliterated pulp chambers

B. white, hypocalcified enamel at the incisal and occlusal thirds * TYPE III - Hypo-maturation *

Karyotype refers to: A. a portion of a chromosome attached to another chromosome B. a pair of chromosomes with an identical extra chromosome C. a microphotograph showing a person's chromosomes from a single cell D. the position occupied by a gene in a chromosome

C. A microphotograph showing a person's chromosomes from a single cell

The Papillon-Lefevre Syndrome is inherited according to an: A. X-linked recessive pattern B. Autosomal-dominant pattern C. Autosomal-recessive pattern D. X-linked dominant pattern

C. Autosomal-recessive pattern

which of the following are the same in mitosis and meiosis? A. the number of chromosomes in each cell at the end B. chiasmata formation between chromosome pairs and crossing over occurs C. before division, the DNA is replicated in S phase D. two rounds of cell division occur

C. Before division, the DNA is replicated in S phase

If a patient with cherubism were to have a jaw lesion biopsied, the histology would closely resemble which the following? A. Odontogenic Keratocyst B. Dentigerous Cyst C. Central Giant Cell Granuloma D. Ameloblastoma

C. Central Giant Cell Granuloma

The constriction that joins the short and long arms of each chromosome is called the: A. Chromatid B. Equatorial plate C. Centromere D. Chiasmata

C. Centromere

Which of the following is the most serious component of Gardner Syndrome? A. Teeth Hypercementosis B. Mandibular Odontomas C. Colorectal Polyposis D. Multiple Osteomas

C. Colorectal Polyposis

.which one of the following is associated with cyclic neutropenia? A. Exfoliating teeth because of short roots B. chipping away of enamel C. diminished number of circulating neutrophils D. premature loss of primary tooth

C. Diminishing number of circulating neutrophils

Which syndromes are caused by nondisjunction? A. Down syndrome B. Klinefelter Syndrome C. Both A and B D. Neither A nor B

C. Down syndrome and Klinefelter syndrome (both A and B)

Patients with hypohidrotic ectodermal dysplasia characteristics have: A. blue sclerae B. excessive amounts of hair C. hypodontia D. multiple tongue nodules

C. Hypodontia (missing teeth)

which of the following is characteristically associated with teeth with large pulp chambers? A. coronal dentin dysplasia B. dentinogensis imperfecta C. Hypophosphatemia D. pitted autosomal-dominant amelogensis imperfecta

C. Hypophosphatemia

Two characteristics clinical component of mandibulofacial dysostosis are: A. lack of clavicles and delayed teeth eruption B. hypodontia and dysplastic nails C. hypoplastic mandible and deafness D. cleft lip and fistulas of lower lip

C. Hypoplastic mandible and deafness

which of the following is characteristically associated with oral ulcerations? A. Gardner Syndrome B. Gorlin Syndrome C. Kostmann Syndrome D. Peutz-Jeghers syndrome

C. Kostmann Syndrome

Deafness is a consistent feature of: A. Leband Syndrome B. Ellis-Van Creveld Syndrome C. Mandibulofacial Dysostosis D. Cherubism

C. Mandibulofacial Dysositis

All of the following are considered components of nevoid basal cell carcinoma syndrome (gorlin syndrome) except one. which is the exception? A. palmar and plantar pitting B. multiple odontogenic keratocysts of the jaw C. multiple osteomas of the jaw D. bifid or splayed ribs

C. Multiple osteomas of the jaw

the most frequent site of hemorrhage in patients with hereditary hemorrhagic telangiectasia is the: A. lip mucosa B. gingiva C. nasal mucosa D. eyelids

C. Nasal Mucosa

A 9-year old boy exhibits markedly swollen, red, and bleeding gingiva. In addition, he has tooth mobility, and the intraoral radiographs show marked alveolar bone atrophy with vertical periodontal pockets. Which one of the following will be found in this child if he were to have papillon-leferve syndrome? A. lack of anterior vestibular sulcus B. Diminished sweating C. Palmar and Plantar Hyperkeratosis D. Blue Sclerae

C. Palmar and Plantar Hyperkeratosis

A 19-year old woman is diagnosed with cleidocranial dysplasia. She has absent clavicles and a mushroom shaped skull. which of the following conditions is she also most likely to have? A. Large pulp chambers B. Taurodontism C. Supernumerary Teeth D. Pegged lateral incisors

C. Supernumerary teeth

Osler-Weber-Rendu Syndrome has all of the following characteristics except one. Which one is the exception? A. Multiple capillary dilations B. Scalp and Ears are affected C. Supernumerary teeth D. Epistaxis

C. Supernumerary teeth

Taurodontic means: A. have long roots B. have a thistle shaped pulp chamber C. are pyramidal in shape D. are supernumerary

C. are pyramidal in shape

odontogenic keratocysts are components of: A. cherubism B. pegged lateral incisors C. Nevoid Basal Cell carcinoma syndrome D. neurofibromatosis of Von Recklinghausen

C. nevoid basal cell carcinoma syndrome

Radiographs of a patient with radicular dentin dysplasia show: A. Taurodontic teeth B. large pulp chambers with long pulp horns C. Pulp chambers with a half-moon appearance D. Internal resorption of teeth

C. pulp chambers with a half-moon appearance

Trisomy refers to: A. One extra chromosomes in each pair B. three extra chromosomes C. The presence of two extra X chromosomes in a male D. a pair of chromosomes with an identical extra chromosomes

D. A pair of chromosomes with an identical extra chromosomes

Patients with hypo-phosphatasisa characteristically have: A. increase in serum alkaline phosphatase levels B. obliterated pulp chambers C. marked gingival keratinization D. absence of root cementum

D. Absence of root cementum

Patients with Trisomy 21 (Down Syndrome) may present with: A. Macroglossia B. Poor Oral Hygiene C. Mental Delay or Disability D. All of the above

D. All of the Above

All of the following are characteristics of Cherubism except one. Which one is the exception? A. Pseudoandontia B. Autosomal Dominant C. Ocular Hypertelorism D. Autosomal recessive

D. Autosomal Recessive

A 14-year old boy is seen in consultation because of bilateral mandibular swelling. Radiographs show a bilateral multi ocular lesion in the ascending mandibular rami. The mother of this patient has similar findings. The most likely diagnosis is: A. Cleidocranial dysplasia B. Gardner Syndrome C. Ellis-Van Creveld Syndrome D. Cherubism

D. Cherubism

In which one of the following conditions can the shoulders be brought forward to the midline as the result of hypo-plastic clavicles? A. Cherubism B. Ellis-Van Creveld Syndrome C. Turner syndrome D. Cleidocranial dysplasia

D. Cleidocranial Dysplasia

Hypotrichosis means: A. increased number of sweat glands B. diminished number of sweat glands C. increased amount of hair D. decreased amount of hair

D. Decreased amount of hair - HYPO: under (decrease) - HYPER: above (increase)

the so called enamel agenesis is one of which type of amelogenesis imperfecta? A. Hypocalcified (Type II) B. Hypomaturation (Type III) C. Hypoplastic-Hypomaturation (Type IV) D. Hypoplastic (Type I)

D. Hypoplastic - Type I

The most frequently exfoliated teeth in patients with hypo-phosphatasia are the: A. Mandibular permanent incisors B. Mandibular Primary Incisors C. Maxillary Primary Molars D. maxillary primary incisors

D. Maxillary Primary Incisors

Hypohidrotic ectodermal dysplasia has all of the following features except one. Which one is the exception? A. Hypotrichosis B. Hypohidrosis C. Saddle Ridge Nose D. Supernumerary teeth

D. Supernumerary teeth

which of the following statements is true when comparing cyclic neutropenia and Kostmann Syndrome? A. the oral lesions in cyclic neutropenia are more severe B. both conditions are inherited as autosomal dominated C. both conditions are associated with capillary fragility. D. the oral lesions in Kostmann syndrome are always present unless systemic treatment is instituted

D. The oral lesions in Kostmann Syndrome are always present unless systemic treatment is instituted

the major concern for a dental hygienist when treating a patient with Osler-Weber-Rendu Syndrome should be: A. severe infections B. epithelial desquamation C. spontaneous ulcerations D. gingival hemorrhage

D. gingival hemorrhage