Pediatric Hematologic Disorders

Willebrand disease

A bleeding disorder caused by low levels of clotting protein in the blood.

neutropenic precautions

Isolation procedures to protect an immunocompromised patient from infections (low neutrophils)

The parent asks the nurse, "I thought the bleeding was stopped. What is causing this pain?" Based on the note (above), how should the nurse reply?

The leftover blood in the shoulder is causing hemarthrosis.

hemophilia A

VIII deficiency

beta thalassemia

abnomrmal hemoglobin chains that lead to RBC destruction

what are some key nursing interventions for hematological disorders ?

adequate oxygen maintining hydration monitor urine output prevent bleeding

what is a key indicator of aplastic anemia

all three blood cellular components are low or absent

A nurse is preparing a teaching plan for a child with hemophilia and his parents. Which information would the nurse be least likely to include to manage a bleeding episode?

apply heat to the site of bleeding

hemarthrosis

blood within a joint

what are some manifestations of beta thalassemia

bone malformations osteoporosis splenomegaly and hepatomegaly yellow or bronze skin pigmentation

The nurse is caring for a child who had a stem cell transplant and is being monitored for engraftment. Which nursing action is priority?

ensure neutropenic precautions are in place

Hemophilia B

factor XI

A child with hemophilia A is scheduled for surgery. Which precautions would the nurse institute with this client?

handle the child carefully when transferring to stretcher

what are some things you will see when your patient is experiencing sickle cell crisis ?

hypoxemia, severe pain from ischemia, dehydration, fever, acidosis

clinical manifesations of von willebrand disease

mucosal bleeding, epistaxis, large bleeding

what are some common interventions for von willebrand disease

nasal packing desmopressin avoid im injections and rectal tem

The nurse is caring for a 4-year-old with sickle cell anemia. A physical finding the nurse might expect to see in him is:

slightly yellow sclerae

what is common with hemophilic disorders

spontaneous and traumatic bleeding due to deficits in coagulating factors

A nurse is providing preoperative care to a child with sickle cell disease. What treatment should the nurse expect to implement prior to surgery?

transfusion of packed RBC's

Deferoxamine is given with

vitamin c to increase efficiency